Pediatric Dentistry management of an 11-day-old patient with cleft palate due to Treacher Collins Syndrome.

Abstract

Introduction: Treacher Collins Syndrome, also called Franceschetti-ZwahlenKlein Syndrome or mandibulofacial dysostosis, characterized by abnormal craniofacial development. Sixty percent of the cases have no family history of this syndrome and if one of the parents is affected with this syndrome, there is a 50% chance of transmitting the gene. Maxillary, zygomatic and mandibular hypoplasia. Temporomandibular joint disorders and stiffness is usually greater in these patients. Conductive hypoplasia and mandibular micrognathia. Cleft palate involvement is a very important factor in terms of breastfeeding and feeding difficulties in these individuals. In some cases, it is recommended to treat mandibular distraction osteogenesis, as well as to guide parents on feeding techniques, prevention of aspiration and if necessary the placement of obturator plates for cleft palate. Objective: To show the preparation, approach and follow-up of a pediatric patient with Treacher Collins syndrome and cleft soft palate and uvula. Case description: A 10 days old male patient came to the Pediatric Dentistry Department of the U.A.Z. for dental care. The clinical examination revealed a fissure in the soft palate at the level of the uvula. She was managed with a modified obturator plate for soft palate. Conclusion: In pediatric dentistry it is up to us to help the patient in the area for which a modified obturator plate was adapted to obstruct part of the fissure.