Benign mucous membrane pemphigoid, unusual clinical manifestation: Pediatric case report

Abstract

Introduction: Benign pemphigoid of the mucous membranes (PMM) is a relatively common autoimmune ampullary disease that often affects the mouth, genitals and eyes, which can cause scars (ocular) and complications if the diagnosis is delayed. It commonly affects adult/elderly patients, with prevalence in women, with rare reports in children. Case report: The case of a 16-year-old patient is reported, who presented as the main symptom “descamación de encías, bled at the head of the teeth”. The extraoral examination and family history did not contribute. An incisional biopsy was performed and the clinicopathological correlation confirmed the diagnosis of PMM. Conclusions: The PMM in pediatric patients presents clinical characteristics similar to those of adult patients. Early diagnosis and treatment of PMM can minimize the risk of complications. The treatment of PMM in children varies depending on the location and the severity of the injury. Mouth lesions respond well to treatment with topical corticosteroids, as occurred in the present case.