Pediatric dentistry under general anesthesia in a patient with Moebius syndrome

Abstract

Introduction: Moebius Syndrome is a congenital neuromuscular disorder characterized by paralysis of the VI and VII cranial nerves. Its prevalence ranges from 0.0002% to 0.002%. Clinical features include strabismus, ophthalmoplegia, ptosis, club foot, microglossia, and malocclusion. Dental treatment under general anesthesia is considered for patients with systemic compromise, lack of cooperation, and/or extensive requirements, highlighting the importance of interdisciplinary collaboration between dentists and medical specialists. Objective: To present a case of an 11-year-old female patient with Moebius Syndrome treated dentally under general anesthesia. Case Presentation: Physical examinations revealed normal temperature, heart rate, blood pressure, weight, and oxygen saturation; cranial nerves III and VI were impaired. The patient had asthma, disorientation in time, space, and person, slight muscular tone rigidity, and clubfoot. Medical Diagnosis: Moebius Syndrome. Dental Diagnosis: 7 active carious lesions, gingivitis, Angle Class II malocclusion with open bite. Treatment: Application of pit and fissure sealants and fluoride varnish, restoration with glass ionomer, and extractions were performed. Specialties involved in care included pediatric dentistry, pediatrics, internal medicine, and anesthesiology. The treatment was conducted during a health campaign organized by Proyecto Mayú in Mérida, Venezuela, with follow-up via tele-dentistry. Conclusion: Successfully providing dental treatment in a hospital setting is feasible, promoting interdisciplinary collaboration and improving patients' quality of life.