Pediatric dental management in a patient with von Willebrand disease: Clinical case

Abstract

Introduction: Von Willebrand disease is the most prevalent hereditary bleeding disorder, characterized by decreased activity of the von Willebrand factor in blood. Its primary function is to mediate platelet adhesion to collagen and stabilize factor VIII, preventing its premature degradation, both essential for primary hemostasis. In dentistry, procedures represent a challange, especially in pediatric patients, due to the risk of prolonged bleeding and the need for interdiciplinary planning. Case report: Preschool patient, 5 years 8 months old, Frankl 3. Biological risk due to von Willebrand disease, cerebral palsy and autism spectrum disorder. Mixed dentition  first phase, high caries risk, with a history of dental caries (dmft: 6). Healthy gingiva, prominent palatal rugae. History of prolonged baby bottle use, interposition of tongue at rest,  phonoarticulation and swallowing. Conclusions: The pediatric dental management of patients with von Willebrand disease presents significant challengues due to the potencial risk of bleeding during clinical procedures. Proper evidence based planning allows for the safe execution of dental treatments without hemorrhagic complications, promoting timely access to care. In pediatric greater, this approach is particularly relevant.