Pediatric dental management of hypoplastic right ventricle syndrome. Keywords: Heart

Abstract

Introduction: Congenital heart disease has a high incidence worldwide. In Mexico, it is the second leading cause of death in children under 5 years of age. Hypoplastic right ventricle syndrome is a rare cyanotic congenital heart disease characterized by underdevelopment of the right ventricle. Case report: This is a 2-year-10-month-old female patient diagnosed with hypoplastic right ventricle syndrome treated with furosemide, spironolactone, and aspirin. She was referred to the pediatric dental service as a protocol for correcting congenital heart disease for cardiac surgery due to the risk of infective endocarditis. A directed examination of the oral cavity revealed primary dentition appropriate for her age and the presence of carious lesions of varying degrees in multiple dental organs. Due to the patient's lack of cooperation due to age, length of treatment, and risk of chairside care due to the underlying diagnosis, it was decided to perform oral rehabilitation using advanced behavioral management under general anesthesia in accordance with the American Heart Association guidelines. Conclusions. For the dental care of patients with hypoplastic right ventricle syndrome, trained pediatric medical and dental personnel are required. The treatment plan should adhere to cardiology guidelines. Specific preventive measures are required to maintain adequate oral health.